Table 2 Case numbers and incidence rates (per million person years) for the hereditary diseases by region of residence
Hereditary autoinflammatory disease (E85.0) | Familial amyloidotic polyneuropathy (FAP, E85.1) | Heredofamilial amyloidosis, unspecified (E85.2) | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|
No. | IR | 95% CI | No. | IR | 95% CI | No. | IR | 95% CI | ||||
Jönköping | 4 | 0.92 | 0.02 | 1.81 | ||||||||
Västerbotten (West Bothnia) | 122 | 45.28 | 37.25 | 53.32 | 4 | 1.29 | 0.03 | 2.55 | ||||
Norrbotten (North Bothnia) | 49 | 13.16 | 9.48 | 16.85 | ||||||||
Unspecified | 102 | 7.96 | 6.42 | 9.51 | ||||||||
All | 210 | 2.83 | 2.45 | 3.22 | 221 | 2.02 | 1.76 | 2.29 | 30 | 0.26 | 0.17 | 0.35 |