Figure 5
Comparison of ΔΨ m of cell lines from patients and controls. The average ΔΨm value of cell lines from patients harboring the tRNAIle A4263G mutation was decreased by 32% compared to control cell lines. ΔΨm values of cell lines from both controls and patients were improved by CsA; control values increased by 33.6%, III-14 values increased by 84.4%, and III-19 values increased by 137.7%.