Table 1 Metabolites in plasma and urine
13 months measurement | 15 months measurement | 17 months measurement | 24 months measurement | Ref. range | |
|---|---|---|---|---|---|
Acylcarnitine in plasma | |||||
C5OH (μmol/L) | 3.88 | 1.66 | 0.53 | 0.37 | 0.07–0.5 |
C0 (μmol/L) | 4.86 | 30.25 | 26.87 | 26.43 | 9.5–50 |
C2 (μmol/L) | 7.99 | 9.87 | 11.88 | 10.27 | 3.4–45 |
C3 (μmol/L) | 4.35 | 0.62 | 1.13 | 1.3 | 0.2–4.5 |
C5OH/C0 | 0.80 | 0.055 | 0.02 | 0.01 | 0–0.02 |
C5OH/C8 | 77.6 | 33.2 | 17.67 | 7.4 | 1.22–18 |
C3/C2 | 0.54 | 0.063 | 0.095 | 0.13 | 0.01–0.2 |
C3/C0 | 0.90 | 0.02 | 0.042 | 0.05 | 0.01–0.2 |
Organic acids in urine | |||||
3-methylcrotonylglycine (μmol/mmol creatinine) | 24.70 | 0.00 | – | 0.00 | 0 |
3-hydroxyisovaleric acid (μmol/mmol creatinine) | 3.63 | 3.00 | – | 1.46 | 0–2.3 |
methylcrotonylglycine (μmol/mmol creatinine) | 17.51 | 0.00 | – | 0.00 | 0 |
acetylglycine (μmol/mmol creatinine) | 6.13 | 0.00 | – | 0.00 | 0–0.1 |
propionylglycine (μmol/mmol creatinine) | 36.71 | 0.00 | – | 0.00 | 0 |
lactic acid (μmol/mmol creatinine) | 247.95 | 4.23 | – | 4.81 | 0–4.7 |
pyruvic acid (μmol/mmol creatinine) | 58.14 | 6.45 | – | 3.42 | 0–24.1 |
3-hydroxybutyric acid (μmol/mmol creatinine) | 966.37 | 2.52 | – | 0.00 | 0–3.7 |
2-keto-3-methyl pentanoic acid (μmol/mmol creatinine) | 6.16 | 0.00 | – | 0.00 | 0 |
2-keto-isocaproic acid (μmol/mmol creatinine) | 6.16 | 0.00 | – | 0.00 | 0 |