PATIENTS | |||||
---|---|---|---|---|---|
N°1 | N°2 | ||||
BLOOD TEST | ONSET | PRESENT | ONSET | PRESENT | NORMAL |
CERULOPLASMIN (gr/dl) | 0.08 | 0.07 | 0.14 | 0.14 | > 0.2 (20) |
SERUM COPPER (μg/dl) | 48 | 13 | 40 | 39 | 80–150 |
URINARY COPPER (μg / 24 h) | 160 | 320 (under Penicillamine) | 120 | 250 (under Penicillamine) | < 40 |
Hb (gr/dl) | 11.3 | 13.7 | 13 | 13.2 | 12–18 |
RBC (Nx106) | 3.9 × 106 | 4.8 × 106 | 4.3 × 106 | 4.4 × 106 | 4–5.5 × 106 |
WBC (Nx103) | 2.5 × 103 | 5.1 × 103 | 5 × 103 | 6 × 103 | 4.8–10.8 × 103 |
PLT (Nx103) | 68 × 103 | 54 × 103 | 242 × 103 | 247 × 103 | 130–400 × 103 |
ALT (U/L) | 33 | 32 | 96 | 151 | 10–35 |
AST (U/L) | 29 | 27 | 51 | 78 | 10–35 |
LDH (U/L) | 554 | 514 | 429 | 277 | 250–500 |
PCE (U/L) | 7000 | 3500 | 8500 | 6000 | 5000–12,000 |
CHOLESTEROL (mg/dl) | 152 | 178 | 207 | 280 | 130–200 |
TRIGLYCERIDS (mg/dl) | 39 | 61 | 237 | 190 | 10–150 |