From: Expanding the spectrum of A20 haploinsufficiency in two Chinese families: cases report
Testing | Case 1 | Case 2 | Case 4 | Normal range | |||
---|---|---|---|---|---|---|---|
Pretherapy | posttherapy | Pretherapy | posttherapy | Pretherapy | posttherapy | ||
ESR (mm/h) | 89.0 | 19 | 35 | 11 | 79.0 | 9.0 | 0–20 |
CRP (mg/dl) | 48.0 | < 8 | 89 | < 8 | 48.0 | < 8 | < 8 |
Hemoglobin (g/dl) | 89.2 | 115.0 | 85.2 | 129.0 | 117 | 142 | 110–160 |
Leukocyte (/mm3) | 3.5 | 6.8 | 11.2 | 13.9 | 13.5 | 13.5 | 4–10 |
Thrombocyte (/mm3) | 81.0 | 118.0 | 205 | 304 | 528 | 238 | 100–300 |
TNF-α(pg/ml) | 22.1 | 4.2 | 0.0–8.1 | ||||
IL-6 | 46.62 | 8.62 | 49.6 | 5.77 | 31.51 | 6.21 | < 7 |
Ferritin | 111.6 | 33.8 | 447.0 | 31.0 | > 2000 | 237.3 | 0.94–71.7 |
C3(g/L) | 0.22 | 0.66 | 1.65 | 1.58 | 1.87 | 1.42 | 0.67–1.76 |
C4(g/L) | 0.06 | 0.1 | 0.56 | 0.72 | 0.3 | 0.36 | 0.1–0.4 |
CH50(U/ml) | 10.0 | 26 | 66 | 58 | 35 | 26 | 23–46 |
ANA | + | + | – | – | + | – | Negative |
Anti-dsDNA | + | – | – | – | – | – | Negative |