Table 1 Patient’s ophthalmological examinations since the age of four
Age | Visual Acuity and Visual Field (RE/LE) | Ophthalmoscopy | VEP | Electroretinogram |
|---|---|---|---|---|
4years–5years | First symptoms: reduction of VA and central VF. VA: 0.08/0.1 (5years) VF: central scotomae BE | Macular alteration with spicules BE | NA | NA |
10year | NA | NA | Abnormal | RE: scotopic: normal, cones response: lower limit of normality. LE: moderate decline of all responses |
12years | VA 0.15/0.15. VF: Loss of the central 20° and 10° RE and LE respectively, conserved peripheral field | Macular atrophy with pigment accumulation BE | NA |