Fam or single patient | Patient | Confirmed mutation carrier | Age at event | Type of event |
---|---|---|---|---|
1 | II-9 | Yes | 54 | Transient ischemic attack |
2 | II-1 | Yes | 55 | Stroke |
II-4 | No* | 49 | ICD† | |
6 | I-2 | No* | 35 | Sudden death |
7 | Yes | 51 | Stroke | |
8 | II-1 | Yes | 49 | Pacemaker (Sick sinus syndrome) |
9 | Yes | 59 | Palpitations, positive EPS‡, ICD† | |
11 | I-2 | No* | 55 | Sudden death |
II-2 | No* | 36 | Sudden death | |
12 | I-1 | No* | 42 | Sudden death |
II-3 | No* | 33 | Sudden death | |
II-6 | Yes | 67 | Inferior MI, coronary heart disease | |
67 | ICD†: Non-sustained VT (holter) | |||
III-3 | Yes | 42 | ICD†: Non-sustained VT (holter) | |
IV-3 | No* | 13 | Sudden death | |
13 | I-1 | No* | 64 | Stroke |
67 | Sudden death | |||
II-1 | No* | 53 | Transient ischemic attack | |
14 | I-1 | No* | 53 | Sudden death |
16 | II-1 | No* | 32 | Sudden death |
II-3 | Yes | 58 | Heart transplantation | |
II-5 | Yes | 61 | Resuscitation due to ventricular fibrillation, ICD† | |
67 | Heart failure related death | |||
III-9 | Yes | 45 | Sudden death | |
17 | II-3 | Yes | 64 | Stroke |
18 | I-2 | No* | 42 | Sudden death |