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Table 4 ERG values of Spanish families with RP1 mutations

From: Three novel and the common Arg677Ter RP1 protein truncating mutations causing autosomal dominant retinitis pigmentosa in a Spanish population

   RODS MIXED (ROD-CONES) CONOS 30 Hz Flicker
INDIVIDUAL EYE b-wave AMPL. b-wave IMP.T a-wave AMPL a-wave IMP.T. b-wave AMPL. b-wave IMP.T b-wave AMP. b-wave IMP.T b-wave AMPL b-wave IMP.T
Q686X            
I-1 R ND ND ND ND ND ND 50 36 NV NV
  L ND ND ND ND ND ND 30 37 NV NV
II-1 R 260 109 378 23 874 49 218 30 131 29
  L 230 105 363 23 833 48 238 31 144 29
II-6 R ND ND ND ND ND ND ND ND ND ND
  L ND ND ND ND ND ND ND ND ND ND
III-6 R 110 93 158 22 389 44 142 31 97 27
  L 157 108 213 22 441 44 140 31 65 25
III-7 R 116 99 197 22 491 45 154 30 68 27
  L 137 94 170 22 412 45 NV NV NV NV
K705fsX712            
II-1 R ND ND 39 24 267 49 85 34 38 32
  L ND ND 51 26 246 52 76 35 63 33
III-1 R - - - - - - - - - -
  L - - - - - - - - - -
III-3 R ND ND ND ND ND ND ND ND ND ND
  L ND ND ND ND ND ND ND ND ND ND
III-4 R 177 93 198 21 492 51 198 29 148 27
  L 187 93 199 21 527 49 230 30 122 27
III-5 R 186 104 221 22 556 47 166 30 58 28
  L 209 109 219 21 500 47 168 30 75 28
III-6 R - - - - - - - - - -
  L - - - - - - - - - -
III-11 R 165 103 274 22 500 46 101 32 77 30
  L 169 106 299 23 563 46 104 31 83 29
III-12 R - - - - - - - - - -
  L - - - - - - - - - -
III-14 R 170 100 266 21 705 49 207 29 127 29
  L 166 103 195 21 570 48 204 29 100 29
IV-1 R 106 86 150 21 393 45 152 29 64 26
  L 138 91 191 21 491 46 193 29 80 27
K722fsX737            
I-1 R - - - - - - - - - -
  L - - - - - - - - - -
II-2, II-3, II-4 R ND ND ND ND ND ND ND ND ND ND
  L ND ND ND ND ND ND ND ND ND ND
  1. ND : Not detectable; NV : Not valid; -:Not done or not available