II:4
|
44
|
F
|
Asymptomatic
|
T wave inversion V1-3
|
None found on echo MRI not done
|
Not performed
|
0
|
2
|
II:7
|
44
|
F
|
Palpitations
|
T wave inversion V1-3
|
Mild right ventricular dilation with wall motion change and aneurismal abnormality on MRI
|
Not performed
|
0
|
3
|
III:2
|
16
|
M
|
Palpitations
|
T wave inversion V1-3 Epsilon wave, V1 VT with LBBB morphology Inducible VT
|
Dilated RV with hypokinetic outflow tract
|
Not performed
|
2
|
2
|
III:3
|
13
|
F
|
Palpitations
|
VT with LBBB morphology
|
Dilated RV with hypokinesia
|
Not performed
|
1
|
2
|
III:4
|
23
|
M
|
Palpitations, chest pain
|
T-wave inversion V1-5 PVCs with LBBB pattern
|
Dilated RV on echo
|
Fibrofatty replacement of RV myocardium on endomyocardial biopsy
|
1
|
4
|
III:6
|
21
|
M
|
Asymptomatic
| |
Dilated RV on echo; Evidence of fatty infiltration of RV wall on MRI
|
Not performed
|
1
|
2
|
III:7
|
19
|
F
|
Syncope
|
Frequent PVCs (>1000/24hrs)
|
Dilated RV on echo and MRI; Fatty infiltration of RV wall on MRI
|
Not performed
|
1
|
4
|
III:9
|
16
|
F
|
Asymptomatic
|
None
|
Mild right ventricular dilation with wall motion change and aneurismal abnormality on MRI
|
Not performed
|
0
|
2
|