Characteristic | CVID (n = 114) | IgGSD (n = 126) |
---|---|---|
Men: Women | 32: 82 | 38: 88 |
Age at Diagnosis, y (range) | 54 ± 16 (21 – 87) | 51 ± 13 (18 – 89) |
Serum Total IgG, mg/dL (range) | 527 ± 115 (140 – 697) | 953 ± 199 (700 – 1751) |
Deficient IgG Subclass(es) | Percentage (n) | Percentage (n) |
1, 3 | 38.6 (44) | 8.7 (11) |
1 | 16.7 (19) | 17.5 (22) |
1, 2, 3 | 12.3 (14) | 0 |
3 | 7.0 (8) | 52.4 (66) |
1, 2 | 7.0 (8) | 0 |
1, 3, 4 | 7.0 (8) | 0 |
1, 4 | 5.3 (6) | 3.2 (4) |
2, 3 | 3.5 (4) | 1.6 (2) |
1, 2, 3, 4 | 2.6 (3) | 0 |
2 | 0.9 (1) | 3.2 (4) |
1, 2, 4 | 0.9 (1) | 0 |
4 | 0 | 7.9 (10) |
3, 4 | 0 | 4.8 (6) |
2, 3, 4 | 0 | 0.8 (1) |
Index Patients with Serum IgA Deficiency, % (n) | 21.1 (24) | 9.5 (12) |
Index Patients with Serum IgM Deficiency, % (n) | 18.4 (21) | 7.9 (10) |