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Table 1 Case numbers and incidence rates (per million person years) for hereditary diseases in Sweden, 2001-2008

From: Incidence of hereditary amyloidosis and autoinflammatory diseases in Sweden: endemic and imported diseases

 

Men

Women

All

Subtype (ICD-10 code)

No.

IR

  95% CI

 

No.

IR

  95% CI

 

No.

IR

  95% CI

 

Hereditary autoinflammatory disease (E85.0)

116

3.11

2.54

3.68

94

2.54

2.03

3.06

210

2.83

2.45

3.22

Familial amyloidotic polyneuropathy (FAP, E85.1)

138

2.35

1.95

2.74

83

1.70

1.33

2.07

221

2.02

1.76

2.29

Heredofamilial amyloidosis, unspecified (E85.2)

15

0.25

0.13

0.38

15

0.27

0.13

0.40

30

0.26

0.17

0.35