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Table 1 Criteria and scoring system for classification of β0-thalassemia/Hb E patients

From: Genetic modifiers of Hb E/β0 thalassemia identified by a two-stage genome-wide association study

Criteria Status Score Status Score Status Score
Hb at steady state, g/dL ≥7.5 0 6.0--7.5 1 <6 2
Age at onset, years >10 0 2--10 0.5 <2 1
Age at 1st transfusion, year >10 0 4--10 1 <4 2
Transfusion requirement Rare/none 0 Occasional 1 Regular 2
Spleen size, cm <3 0 3--10 1 >10 2
Splenectomy No 0 Yes 2