Countries
|
Number of MJD
|
Number of SCA
|
Frequency (%)
|
Reference
|
---|
Portugal
|
32
|
38
|
84.2
|
16
|
Brazil
|
96
|
114
|
84.2
|
17
|
Present study
|
100
|
138
|
72.5
| |
Portugal/Brazil
|
67
|
106
|
63.2
|
44
|
Germany
|
32
|
77
|
41.6
|
45
|
France
|
25
|
87
|
28.7
|
46
|
Holland
|
64
|
227
|
28.2
|
47
|
America*
|
31
|
149
|
20.8
|
48
|
Spain
|
11
|
72
|
15.3
|
49
|
Australia
|
11
|
88
|
12.5
|
13
|
Mexico
|
13
|
108
|
12.0
|
50
|
South Africa
|
2
|
54
|
3.7
|
51
|
Italy
|
2
|
183
|
1.1
|
52
|
UK
|
0
|
22
|
0
|
53
|
Serbia
|
0
|
38
|
0
|
54
|
Finland
|
0
|
49
|
0
|
55
|
Norway
|
0
|
19
|
0
|
56
|
Czech
|
0
|
118#
|
0
|
11
|
Combined
|
486
|
1687
|
28.8
| |
- *The patient subjects mixed with African American, Caucasian American, Cambodian, Japanese, Pakistani, Lebanese and Peruvian; # composed of patients with dominant SCA and sporadic ataxia