Origin | Series | n | % Females | % Definite diagnosis | Median age (range) | PRNP M129V genotype | ||
---|---|---|---|---|---|---|---|---|
MM n (%) | MV n (%) | VV n (%) | ||||||
NL | sCJD | 79 | 59 | 52 | 67 (34–87) | 48 (67) | 16 (22) | 8 (11) |
controls | 309 | 56 | N/A | 71 (55–93) | 135 (45) | 145 (48) | 23 (8) | |
UK | sCJD | 48 | 58 | 50 | 67 (49–81) | 22 (46) | 13 (27) | 13 (27) |
vCJD | 52 | 31 | 74 | 25 (12–62) | 52 (100) | 0 (0) | 0 (0) | |
Italy | sCJD | 194 | 57 | 73 | 67 (35–87) | 141 (73) | 31 (16) | 22 (11) |