From: Polymorphisms in the glutathione pathway modulate cystic fibrosis severity: a cross-sectional study
Variable | Without taking CFTRmutation into account | No CFTRmutations identified | No CFTRmutations identified with PI | One identified CFTRmutation | One identified CFTRmutation with PI | Two identified CFTRmutations | ||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|
p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | |
Gendera | 0.753 | 1 | 0.532 | 1 | 1 | 1 | 0.149 | 0.596 | 0.510 | 1 | 0.824 | 1 |
Agea | 0.057 | 0.228 | 0.710 | 1 | 0.245 | 0.980 | 0.541 | 1 | 1 | 1 | 0.339 | 1 |
Onset of symptomsa | 1 | 1 | 1 | 1 | 0.420 | 1 | 0.731 | 1 | 0.078 | 0.312 | 0.812 | 1 |
Onset of pulmonary diseasea | 0.507 | 1 | 1 | 1 | 0.152 | 0.608 | 0.727 | 1 | 0.302 | 1 | 0.816 | 1 |
Onset of digestive diseasea | 0.865 | 1 | 0.646 | 1 | 0.408 | 1 | 1 | 1 | 0.158 | 0.632 | 1 | 1 |
Diagnosisa | 0.335 | 1 | 0.419 | 1 | 1 | 1 | 0.330 | 1 | 1 | 1 | 1 | 1 |
BMIa | 1 | 1 | 1 | 1 | 0.281 | 1 | 0.704 | 1 | 0.709 | 1 | 0.785 | 1 |
Bhalla scoreb | 0.35 | 1 | 0.830 | 1 | 0.468 | 1 | 0.169 | 0.676 | 0.833 | 1 | 0.495 | 1 |
Kanga scoreb | 0.011 | 0.044 | 0.734 | 1 | 0.788 | 0.067 | 0.268 | 0.588 | 1 | 0.027 | 0.108 | |
Shwachman-Kulczycki scoreb | 0.091 | 0.364 | 0.725 | 1 | 0.223 | 0.892 | 0.034 | 0.136 | 0.545 | 1 | 0.159 | 0.636 |
Nasal polyposisa | 0.688 | 1 | 0.251 | 1 | 0.555 | 1 | 0.692 | 1 | 1 | 1 | 0.083 | 0.332 |
Diabetes mellitusa | 0.688 | 1 | 1 | 1 | 1 | 1 | 0.419 | 1 | 0.217 | 0.868 | 1 | 1 |
Osteoporosisa | 0.133 | 0.532 | 1 | 1 | 0.068 | 0.272 | 0.25 | 1 | 0.630 | 1 | 0.335 | |
Meconium ileus | 1 | 1 | 1 | 1 | 0.304 | 1 | 1 | 1 | 0.417 | 1 | 1 | 1 |
Pancreatic insufficiencya | 0.698 | 1 | 0.180 | 0.720 | - | - | 0.376 | 1 | - | - | 1 | 1 |
SpO2b | 0.033 | 0.132 | 0.234 | 0.936 | 0.142 | 0.568 | 0.548 | 1 | 0.134 | 0.536 | 0.149 | 0.596 |
FVC(%)b | 0.412 | 1 | 0.944 | 1 | 0.061 | 0.244 | 0.036 | 0.144 | 0.755 | 1 | 0.955 | 1 |
FEV1(%)b | 0.166 | 0.664 | 0.877 | 1 | 0.094 | 0.376 | 0.030 | 0.120 | 0.381 | 1 | 0.577 | 1 |
FEV1/FVCb | 0.054 | 0.216 | 0.912 | 1 | 0.403 | 1 | 0.050 | 0.200 | 0.247 | 0.988 | 0.111 | |
FEF25–75%b | 0.061 | 0.244 | 0.934 | 1 | 0.177 | 0.708 | 0.029 | 0.116 | 0.577 | 1 | 0.272 | 1 |
First P. aeruginosa a | 0.350 | 1 | 0.453 | 1 | 0.433 | 1 | 0.716 | 1 | 0.015 | 0.060 | 0.799 | 1 |
P. aeruginosa mucoida | 0.152 | 0.608 | 1 | 1 | 0.443 | 1 | 0.064 | 0.256 | 0.178 | 0.712 | 0.371 | 1 |
P. aeruginosa no mucoida | 0.057 | 0.228 | 1 | 1 | 0.243 | 0.972 | 0.003 | 0.012 | 0.023 | 0.092 | 0.351 | 1 |
A. xylosoxidans a | 0.187 | 0.748 | 0.066 | 0.044 | 0.176 | 0.565 | 1 | 1 | 1 | 0.343 | 1 | |
S. aureus a | 0.849 | 1 | 0.708 | 1 | 1 | 1 | 0.376 | 1 | 0.024 | 0.096 | 0.394 | 1 |
B. cepacia a | 0.246 | 0.984 | 1 | 1 | 1 | 1 | 0.471 | 1 | 0.082 | 0.328 | 0.394 | 1 |