From: Polymorphisms in the glutathione pathway modulate cystic fibrosis severity: a cross-sectional study
Variable | Without taking CFTRmutation into account | No CFTRmutations identified | No CFTRmutations identified with PI | One identified CFTRmutation | One identified CFTRmutation with PI | Two identified CFTRmutations | ||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|
p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | p-value | p-corrected | |
Gendera | 0.550 | 1 | 0.396 | 1 | 1 | 1 | 0.267 | 1 | 0.763 | 1 | 0.184 | 0.736 |
Agea | 0.011 | 0.044 | 0.750 | 1 | 0.500 | 1 | 0.051 | 0.204 | 1 | 1 | 0.058 | 0.232 |
Onset of symptomsa | 0.876 | 1 | 0.473 | 1 | 0.720 | 1 | 1 | 1 | 0.531 | 1 | 1 | 1 |
Onset of pulmonary diseasea | 0.754 | 1 | 0.729 | 1 | 0.252 | 1 | 0.757 | 1 | 0.757 | 1 | 1 | 1 |
Onset of digestive diseasea | 0.516 | 1 | 1 | 1 | 0.462 | 1 | 0.761 | 1 | 1 | 1 | 1 | 1 |
Diagnosisa | 0.644 | 1 | 0.694 | 1 | 0.185 | 0.740 | 0.561 | 1 | 0.763 | 1 | 0.441 | 1 |
BMIa | 0.856 | 1 | 0.331 | 1 | 1 | 1 | 1 | 1 | 0.488 | 1 | 1 | 1 |
Bhalla scoreb | 0.098 | 0.392 | 0.187 | 1 | 0.671 | 1 | 0.491 | 1 | 0.098 | 0.392 | 0.392 | 1 |
Kanga scoreb | 0.716 | 1 | 0.867 | 1 | 0.604 | 1 | 0.407 | 1 | 0.416 | 1 | 0.300 | 1 |
Shwachman-Kulczycki scoreb | 0.554 | 1 | 0.984 | 1 | 0.121 | 0.484 | 0.73 | 1 | 0.198 | 0.792 | 0.170 | 0.680 |
Nasal polyposisa | 0.848 | 1 | 0.306 | 1 | 0.601 | 1 | 1 | 1 | 0.412 | 1 | 0.562 | 1 |
Diabetes mellitusa | 0.336 | 1 | 1 | 1 | 1 | 1 | 0.703 | 1 | 1 | 1 | 0.582 | 1 |
Osteoporosisa | 0.159 | 0.318 | 0.715 | 0.953 | 1 | 1 | 0.345 | 1 | 0.009 | 0.036 | ||
Meconium ileus | 0.403 | 1 | 1 | 1 | 0.398 | 1 | 1 | 1 | 0.457 | 1 | 0.161 | 0.644 |
Pancreatic insufficiencya | 0.581 | 1 | 0.393 | 1 | 0.187 | 0.748 | 0.703 | 1 | - | - | 0.578 | 1 |
SpO2b | 0.967 | 1 | 0.839 | 1 | 0.230 | 0.920 | 0.156 | 0.624 | 0.157 | 0.628 | 0.346 | 1 |
FVC(%)b | 0.441 | 1 | 0.407 | 1 | 0.279 | 1 | 0.849 | 1 | 0.315 | 1 | 0.626 | 1 |
FEV1(%)b | 0.338 | 1 | 0.467 | 1 | 0.923 | 1 | 0.907 | 1 | 0.221 | 0.884 | 0.451 | 1 |
FEV1/FVCb | 0.295 | 1 | 0.265 | 1 | 0.218 | 0.872 | 0.575 | 1 | 0.771 | 1 | 0.439 | 1 |
FEF25–75%b | 0.146 | 0.584 | 0.498 | 1 | 0.261 | 1 | 0.505 | 1 | 0.379 | 1 | 0.291 | 1 |
First P. aeruginosa a | 0.035 | 0.140 | 1 | 1 | 0.473 | 1 | 0.056 | 0.224 | 1 | 1 | 0.203 | 0.812 |
P. aeruginosa mucoida | 0.289 | 1 | 0.331 | 1 | 0.505 | 1 | 0.782 | 1 | 0.760 | 1 | 0.653 | 1 |
P. aeruginosa no mucoida | 1 | 1 | 0.548 | 1 | 1 | 1 | 0.776 | 1 | 0.760 | 1 | 0.482 | 1 |
A. xylosoxidans a | 0.806 | 1 | 0.196 | 0.784 | 1 | 1 | 0.350 | 1 | 0.488 | 1 | 0.755 | 1 |
S. aureus a | 0.721 | 1 | 0.507 | 1 | 1 | 1 | 0.743 | 1 | 0.185 | 0.740 | 0.565 | 1 |
B. cepacia a | 0.667 | 1 | 0.196 | 0.784 | 1 | 1 | 0.703 | 1 | 0.698 | 1 | 0.404 | 1 |